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    Anaesthetic management of a patient with familial normokalaemic periodic paralysis.

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    Authors
    Walsh, F
    Kelly, D
    Affiliation
    Department of Anaesthesia, Cork University Hospital, Wilton, Ireland.
    Issue Date
    2012-02-03T15:15:37Z
    MeSH
    Anesthesia/*methods
    Child, Preschool
    Humans
    Male
    Paralyses, Familial Periodic/*physiopathology
    Potassium/blood
    
    Metadata
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    Citation
    Can J Anaesth. 1996 Jul;43(7):684-6.
    Journal
    Canadian journal of anaesthesia = Journal canadien d'anesthesie
    URI
    http://hdl.handle.net/10147/209226
    DOI
    10.1007/BF03017951
    PubMed ID
    8807173
    Abstract
    PURPOSE: We describe the anaesthetic management of a patient with the autosomal dominant inherited disease, normokalaemic periodic paralysis. The disease results in intermittent bouts of limb and respiratory muscular weakness in association with hypothermia, stress, prolonged fasting or exercise. Unlike hypokalaemic and hyperkalaemic periodic paralysis, the more common variants of the disease, normokalaemic periodic paralysis is not accompanied by alterations in the plasma potassium concentration. CLINICAL FEATURES: A five-year-old boy presented for emergency scrotal exploration. He had a family history of periodic paralysis and had experienced previous episodes of weakness, two of which had required hospitalization for respiratory distress. On admission there was no evidence of weakness and serum potassium concentration was 4.2 mMol.L-1. A spinal anaesthetic was performed and the procedure was uncomplicated by muscle paralysis above the level of the spinal block. CONCLUSION: Avoidance of known precipitating factors and judicious use of neuromuscular blocking drugs has been advocated in patients with this disorder presenting for surgery. In appropriate circumstances, spinal anaesthesia represents a useful option in patients with normokalaemic periodic paralysis.
    Language
    eng
    ISSN
    0832-610X (Print)
    0832-610X (Linking)
    ae974a485f413a2113503eed53cd6c53
    10.1007/BF03017951
    Scopus Count
    Collections
    Cork University Hospital

    entitlement

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