Anaesthesia for caesarean section in a patient with Sturge-Weber syndrome following acute neurological deterioration.
AffiliationDepartment of Anaesthesia, The Rotunda Hospital, Dublin, Ireland.
Anaesthesia , Obstetrical
Magnetic Resonance Imaging
Nervous System Diseases
MetadataShow full item record
CitationAnaesthesia for caesarean section in a patient with Sturge-Weber syndrome following acute neurological deterioration. 2011, 20 (3):259-62 Int J Obstet Anesth
JournalInternational journal of obstetric anesthesia
AbstractSturge-Weber syndrome consists of facial capillary malformation (port-wine stain) and abnormal blood vessels in the brain or eye. Seizures, developmental delay and intracranial and airway angiomata are principal concerns. We report a 28-year-old primiparous woman at 41 weeks of gestation with Sturge-Weber syndrome who developed unilateral weakness, aphasia, blurred vision and confusion. Preeclampsia was excluded. Neuroimaging showed left sided cerebral oedema and a right parieto-occipital lesion, most likely an angioma. Caesarean section was planned to avoid the risk of angioma rupture during labour. General anesthesia was avoided due to the haemodynamic response to laryngoscopy and reports of seizure-related mortality. Despite the possibility of raised intracranial pressure and precipitation of cerebral herniation, a lumbar epidural block was administered but failed. A subarachnoid block was successfully performed and a healthy infant delivered. The choice of anaesthesia was strongly influenced by detailed radiological investigations and multidisciplinary participation.
Item TypeArticle In Press
- Retrospective review of screening for Sturge-Weber syndrome with brain magnetic resonance imaging and electroencephalography in infants with high-risk port-wine stains.
- Authors: Zallmann M, Mackay MT, Leventer RJ, Ditchfield M, Bekhor PS, Su JC
- Issue date: 2018 Sep
- The Bone Does Not Predict the Brain in Sturge-Weber Syndrome.
- Authors: Warne RR, Carney OM, Wang G, Bhattacharya D, Chong WK, Aylett SE, Mankad K
- Issue date: 2018 Aug
- Sturge-Weber syndrome.
- Authors: Baselga E
- Issue date: 2004 Jun
- Sturge-Weber syndrome accompanied with multiple congenital intracranial lesions.
- Authors: Ergün R, Okten AI, Gezercan Y, Gezici AR
- Issue date: 2007 Aug
- Central hypothyroidism and Sturge-Weber syndrome.
- Authors: Comi AM, Bellamkonda S, Ferenc LM, Cohen BA, Germain-Lee EL
- Issue date: 2008 Jul