An unusual cause of spontaneous pneumothorax: the Mounier-Kuhn syndrome.
Kent, B D Sulaiman, I Akasheh, N B Nadarajan, P Moloney, E Lane, S J
Kent, B D
Sulaiman, I
Akasheh, N B
Nadarajan, P
Moloney, E
Lane, S J
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Date
2012-02-01T10:29:19Z
Date Submitted
Keywords
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Subject Mesh
Female
Humans
Lung/*radiography
Middle Aged
Pneumothorax/*etiology/radiography
Tracheobronchomegaly/complications/*radiography
Humans
Lung/*radiography
Middle Aged
Pneumothorax/*etiology/radiography
Tracheobronchomegaly/complications/*radiography
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Abstract
We present the case of a 54-year old woman referred to our service with an unusual presentation of an under-diagnosed condition. A life-long non-smoker, she was referred to respiratory services by our emergency department with a left sided pneumothorax, progressive dyspnoea on exertion, and recurrent chest infections. Subsequent investigation yielded findings consistent with Mounier-Kuhn syndrome (Tracheobronchomegaly), a condition characterised by marked dilatation of the proximal airways, recurrent chest infection, and consequent emphysema and bronchiectasis. Although rarely diagnosed, some degree of Mounier-Kuhn syndrome may occur in up to 1 in 500 adults.
Language
eng
Citation
ISSN
0332-3102 (Print)
0332-3102 (Linking)
0332-3102 (Linking)
eISSN
ISBN
DOI
PMID
21736094