Sternoplasty and rib distraction in neonatal Jeune syndrome.

Hdl Handle:
http://hdl.handle.net/10147/263324
Title:
Sternoplasty and rib distraction in neonatal Jeune syndrome.
Authors:
Conroy, Eimear; Eustace, Nicholas; McCormack, Damian
Affiliation:
Departments of Paediatric Orthopaedic Surgery, Children's University Hospital, Temple Street, Dublin, Ireland. eimearconroy04@eircom
Citation:
Sternoplasty and rib distraction in neonatal Jeune syndrome. 2010, 30 (6):527-30 J Pediatr Orthop
Journal:
Journal of pediatric orthopedics
Issue Date:
Sep-2010
URI:
http://hdl.handle.net/10147/263324
DOI:
10.1097/BPO.0b013e3181e03a08
PubMed ID:
20733414
Abstract:
A 12-week-old boy with Jeune syndrome (asphyxiating thoracic dystrophy) was referred to the orthopaedic unit with progressive respiratory failure, recurrent respiratory tract infections, and recurrent admissions to the intensive care unit for ventilatory support. His chest x-ray revealed a small and narrow thoracic cage with short broad ribs and abnormal costal cartilages. His chest expansion was impaired by the short, horizontally positioned ribs resulting in alveolar hypoventilation. Without surgical intervention to expand his thoracic cage, he would die of respiratory failure.
Item Type:
Article
Language:
en
MeSH:
Ellis-Van Creveld Syndrome; Follow-Up Studies; Humans; Infant; Male; Osteogenesis, Distraction; Respiratory Insufficiency; Ribs; Sternum; Thoracic Wall
ISSN:
1539-2570

Full metadata record

DC FieldValue Language
dc.contributor.authorConroy, Eimearen_GB
dc.contributor.authorEustace, Nicholasen_GB
dc.contributor.authorMcCormack, Damianen_GB
dc.date.accessioned2012-12-20T10:28:47Z-
dc.date.available2012-12-20T10:28:47Z-
dc.date.issued2010-09-
dc.identifier.citationSternoplasty and rib distraction in neonatal Jeune syndrome. 2010, 30 (6):527-30 J Pediatr Orthopen_GB
dc.identifier.issn1539-2570-
dc.identifier.pmid20733414-
dc.identifier.doi10.1097/BPO.0b013e3181e03a08-
dc.identifier.urihttp://hdl.handle.net/10147/263324-
dc.description.abstractA 12-week-old boy with Jeune syndrome (asphyxiating thoracic dystrophy) was referred to the orthopaedic unit with progressive respiratory failure, recurrent respiratory tract infections, and recurrent admissions to the intensive care unit for ventilatory support. His chest x-ray revealed a small and narrow thoracic cage with short broad ribs and abnormal costal cartilages. His chest expansion was impaired by the short, horizontally positioned ribs resulting in alveolar hypoventilation. Without surgical intervention to expand his thoracic cage, he would die of respiratory failure.en_GB
dc.language.isoenen
dc.rightsArchived with thanks to Journal of pediatric orthopedicsen_GB
dc.subject.meshEllis-Van Creveld Syndrome-
dc.subject.meshFollow-Up Studies-
dc.subject.meshHumans-
dc.subject.meshInfant-
dc.subject.meshMale-
dc.subject.meshOsteogenesis, Distraction-
dc.subject.meshRespiratory Insufficiency-
dc.subject.meshRibs-
dc.subject.meshSternum-
dc.subject.meshThoracic Wall-
dc.titleSternoplasty and rib distraction in neonatal Jeune syndrome.en_GB
dc.typeArticleen
dc.contributor.departmentDepartments of Paediatric Orthopaedic Surgery, Children's University Hospital, Temple Street, Dublin, Ireland. eimearconroy04@eircomen_GB
dc.identifier.journalJournal of pediatric orthopedicsen_GB
dc.description.provinceLeinsteren
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