Case report: unusual dental morphology in a child with ankyloblepharon-ectodermal defects-cleft lip/palate (AEC) syndrome.

Hdl Handle:
http://hdl.handle.net/10147/207459
Title:
Case report: unusual dental morphology in a child with ankyloblepharon-ectodermal defects-cleft lip/palate (AEC) syndrome.
Authors:
Fitzgerald, K; Lynch, S A; McKiernan, E
Affiliation:
Dept of Paediatric Dentistry, Our Lady's Children's Hospital, Crumlin, Dublin 12,, Ireland. kirsten.fitzgerald@olchc.ie
Citation:
Eur Arch Paediatr Dent. 2011 Aug;12(4):219-23.
Journal:
European archives of paediatric dentistry : official journal of the European, Academy of Paediatric Dentistry
Issue Date:
1-Feb-2012
URI:
http://hdl.handle.net/10147/207459
PubMed ID:
21806908
Abstract:
BACKGROUND: Anomalies of dental anatomy are common in the ectodermal dysplasia syndromes. These anomalies, when found in combination with dental caries, can pose a restorative challenge for the paediatric dentist. Modification of traditional techniques and approaches may help the practitioner provide a successful treatment outcome. CASE REPORT: A 3 years and 11 months old girl with a diagnosis of ankyloblepharon-ectodermal dysplasiacleft lip/palate (AEC) syndrome was referred for treatment to a specialist paediatric dental service. Her abnormal dental anatomy, hypodontia and dental caries formed a triad of challenges for the team. Under general anaesthesia, her dentition was restored using a combination of restorative approaches and techniques, including the placement of both composite resin and preformed metal crown restorations. FOLLOW-UP: At 18-month followup, the family had successfully implemented good home care and dietary practices, and the local dental service had instituted a preventive programme consisting of regular examination, advice and fluoride varnish placement. The restorations remained intact and no further caries was detected. At 24-month follow-up, the first permanent molars were partially erupted, and displayed unusually deep fissures. There was also a degree of ectopic eruption of the first permanent molars, and possibly of one of the maxillary permanent incisors. CONCLUSION: Dental care for children with AEC syndrome is optimised by early intervention, good home care and regular professional review. Dental care providers should be aware of the possibility of complex dental anatomy, and bear this in mind should it become necessary to formulate a restorative treatment plan.
Language:
eng
MeSH:
Child, Preschool; Cleft Lip/*complications; Cleft Palate/*complications; Crowns; Dental Caries/therapy; Dental Restoration, Permanent/methods; Ectodermal Dysplasia/*complications; Eye Abnormalities/*complications; Eyelids/abnormalities; Female; Humans; Tooth Abnormalities/*etiology
ISSN:
1818-6300 (Print); 1818-6300 (Linking)

Full metadata record

DC FieldValue Language
dc.contributor.authorFitzgerald, Ken_GB
dc.contributor.authorLynch, S Aen_GB
dc.contributor.authorMcKiernan, Een_GB
dc.date.accessioned2012-02-01T10:25:33Z-
dc.date.available2012-02-01T10:25:33Z-
dc.date.issued2012-02-01T10:25:33Z-
dc.identifier.citationEur Arch Paediatr Dent. 2011 Aug;12(4):219-23.en_GB
dc.identifier.issn1818-6300 (Print)en_GB
dc.identifier.issn1818-6300 (Linking)en_GB
dc.identifier.pmid21806908en_GB
dc.identifier.urihttp://hdl.handle.net/10147/207459-
dc.description.abstractBACKGROUND: Anomalies of dental anatomy are common in the ectodermal dysplasia syndromes. These anomalies, when found in combination with dental caries, can pose a restorative challenge for the paediatric dentist. Modification of traditional techniques and approaches may help the practitioner provide a successful treatment outcome. CASE REPORT: A 3 years and 11 months old girl with a diagnosis of ankyloblepharon-ectodermal dysplasiacleft lip/palate (AEC) syndrome was referred for treatment to a specialist paediatric dental service. Her abnormal dental anatomy, hypodontia and dental caries formed a triad of challenges for the team. Under general anaesthesia, her dentition was restored using a combination of restorative approaches and techniques, including the placement of both composite resin and preformed metal crown restorations. FOLLOW-UP: At 18-month followup, the family had successfully implemented good home care and dietary practices, and the local dental service had instituted a preventive programme consisting of regular examination, advice and fluoride varnish placement. The restorations remained intact and no further caries was detected. At 24-month follow-up, the first permanent molars were partially erupted, and displayed unusually deep fissures. There was also a degree of ectopic eruption of the first permanent molars, and possibly of one of the maxillary permanent incisors. CONCLUSION: Dental care for children with AEC syndrome is optimised by early intervention, good home care and regular professional review. Dental care providers should be aware of the possibility of complex dental anatomy, and bear this in mind should it become necessary to formulate a restorative treatment plan.en_GB
dc.language.isoengen_GB
dc.subject.meshChild, Preschoolen_GB
dc.subject.meshCleft Lip/*complicationsen_GB
dc.subject.meshCleft Palate/*complicationsen_GB
dc.subject.meshCrownsen_GB
dc.subject.meshDental Caries/therapyen_GB
dc.subject.meshDental Restoration, Permanent/methodsen_GB
dc.subject.meshEctodermal Dysplasia/*complicationsen_GB
dc.subject.meshEye Abnormalities/*complicationsen_GB
dc.subject.meshEyelids/abnormalitiesen_GB
dc.subject.meshFemaleen_GB
dc.subject.meshHumansen_GB
dc.subject.meshTooth Abnormalities/*etiologyen_GB
dc.titleCase report: unusual dental morphology in a child with ankyloblepharon-ectodermal defects-cleft lip/palate (AEC) syndrome.en_GB
dc.contributor.departmentDept of Paediatric Dentistry, Our Lady's Children's Hospital, Crumlin, Dublin 12,, Ireland. kirsten.fitzgerald@olchc.ieen_GB
dc.identifier.journalEuropean archives of paediatric dentistry : official journal of the European, Academy of Paediatric Dentistryen_GB
dc.description.provinceLeinster-

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