The management of thoracic inlet syndrome associated with Hurler's syndrome: a novel surgical technique.

Hdl Handle:
http://hdl.handle.net/10147/207429
Title:
The management of thoracic inlet syndrome associated with Hurler's syndrome: a novel surgical technique.
Authors:
Ahsan, Rauf M; Early, Sarah A; O'Meara, Anne; Nolke, Lars
Affiliation:
Department of Cardiothoracic Surgery, Our Lady's Children's Hospital, Crumlin,, Dublin 12, Ireland.
Citation:
Eur J Cardiothorac Surg. 2009 Dec;36(6):1081-3. Epub 2009 Oct 28.
Journal:
European journal of cardio-thoracic surgery : official journal of the European, Association for Cardio-thoracic Surgery
Issue Date:
1-Feb-2012
URI:
http://hdl.handle.net/10147/207429
DOI:
10.1016/j.ejcts.2009.05.055
PubMed ID:
19864154
Abstract:
A 21-year-old male developed significant swelling of his tongue after a respiratory arrest. The patient had a history of Hurler's syndrome. Magnetic resonance imaging (MRI) angiogram delineated that the swelling was due to compression of his internal jugular veins at the level of the first rib, resulting in thoracic inlet obstruction. The standard surgical treatment of thoracic inlet obstruction was not suitable in this patient's case due to his short thick neck and his characteristic Hurler's syndrome body habitus. Therefore, a novel surgical strategy was used to decompress his head and neck vessels. The manubrium was widened using an iliac crest bone graft, stabilised using internal fixation plates and reconstructed with a pectoral muscle flap.
Language:
eng
MeSH:
Airway Obstruction/etiology; Bone Transplantation/methods; Constriction, Pathologic/complications/surgery; Decompression, Surgical/methods; Humans; Jugular Veins/pathology/*surgery; Macroglossia/etiology; Male; Manubrium/surgery; Mucopolysaccharidosis I/*surgery; Thoracic Outlet Syndrome/*surgery; Young Adult
ISSN:
1873-734X (Electronic); 1010-7940 (Linking)

Full metadata record

DC FieldValue Language
dc.contributor.authorAhsan, Rauf Men_GB
dc.contributor.authorEarly, Sarah Aen_GB
dc.contributor.authorO'Meara, Anneen_GB
dc.contributor.authorNolke, Larsen_GB
dc.date.accessioned2012-02-01T10:24:47Z-
dc.date.available2012-02-01T10:24:47Z-
dc.date.issued2012-02-01T10:24:47Z-
dc.identifier.citationEur J Cardiothorac Surg. 2009 Dec;36(6):1081-3. Epub 2009 Oct 28.en_GB
dc.identifier.issn1873-734X (Electronic)en_GB
dc.identifier.issn1010-7940 (Linking)en_GB
dc.identifier.pmid19864154en_GB
dc.identifier.doi10.1016/j.ejcts.2009.05.055en_GB
dc.identifier.urihttp://hdl.handle.net/10147/207429-
dc.description.abstractA 21-year-old male developed significant swelling of his tongue after a respiratory arrest. The patient had a history of Hurler's syndrome. Magnetic resonance imaging (MRI) angiogram delineated that the swelling was due to compression of his internal jugular veins at the level of the first rib, resulting in thoracic inlet obstruction. The standard surgical treatment of thoracic inlet obstruction was not suitable in this patient's case due to his short thick neck and his characteristic Hurler's syndrome body habitus. Therefore, a novel surgical strategy was used to decompress his head and neck vessels. The manubrium was widened using an iliac crest bone graft, stabilised using internal fixation plates and reconstructed with a pectoral muscle flap.en_GB
dc.language.isoengen_GB
dc.subject.meshAirway Obstruction/etiologyen_GB
dc.subject.meshBone Transplantation/methodsen_GB
dc.subject.meshConstriction, Pathologic/complications/surgeryen_GB
dc.subject.meshDecompression, Surgical/methodsen_GB
dc.subject.meshHumansen_GB
dc.subject.meshJugular Veins/pathology/*surgeryen_GB
dc.subject.meshMacroglossia/etiologyen_GB
dc.subject.meshMaleen_GB
dc.subject.meshManubrium/surgeryen_GB
dc.subject.meshMucopolysaccharidosis I/*surgeryen_GB
dc.subject.meshThoracic Outlet Syndrome/*surgeryen_GB
dc.subject.meshYoung Adulten_GB
dc.titleThe management of thoracic inlet syndrome associated with Hurler's syndrome: a novel surgical technique.en_GB
dc.contributor.departmentDepartment of Cardiothoracic Surgery, Our Lady's Children's Hospital, Crumlin,, Dublin 12, Ireland.en_GB
dc.identifier.journalEuropean journal of cardio-thoracic surgery : official journal of the European, Association for Cardio-thoracic Surgeryen_GB
dc.description.provinceLeinster-

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