Fulminant limb and retroperitoneal necrotizing fasciitis in a 15-year-old girl with Fanconi anaemia.

Hdl Handle:
http://hdl.handle.net/10147/206376
Title:
Fulminant limb and retroperitoneal necrotizing fasciitis in a 15-year-old girl with Fanconi anaemia.
Authors:
O'Regan, Kevin; O'Mahony, Edward; MacEneaney, Peter; Fitzgerald, Edward; Maher, Michael M
Affiliation:
Department of Radiology, Mercy University Hospital, Cork, Republic of Ireland., kevin.oregan@ucc.ie
Citation:
Pediatr Radiol. 2009 Oct;39(10):1095-7. Epub 2009 Jun 23.
Journal:
Pediatric radiology
Issue Date:
31-Jan-2012
URI:
http://hdl.handle.net/10147/206376
DOI:
10.1007/s00247-009-1324-4
PubMed ID:
19547962
Abstract:
Necrotizing fasciitis (NF) is an uncommon soft-tissue infection in children that carries a high mortality rate. We present a 15-year-old girl with chronic pancytopenia secondary to Fanconi anaemia who developed extensive NF of the lower limb, which unfortunately resulted in a fatal outcome. Immunodeficiency is a known risk factor for the development of this condition. The findings in this case demonstrate that patients with Fanconi anaemia may be susceptible to NF and that the clinical course may be more aggressive due to underlying immunosuppression. Prompt diagnosis of NF is vital in order to initiate appropriate treatment and to optimize patient outcome. Radiological investigation demonstrated extensive soft-tissue gas and destruction affecting the entire lower limb, abdominal wall and retroperitoneum, which led to timely definitive diagnosis and management.
Language:
eng
MeSH:
Adolescent; Fanconi Anemia/*complications/*radiography; Fasciitis, Necrotizing/*complications/*radiography; Fatal Outcome; Female; Humans; Leg/*radiography; Retroperitoneal Space/*radiography
ISSN:
1432-1998 (Electronic); 0301-0449 (Linking)

Full metadata record

DC FieldValue Language
dc.contributor.authorO'Regan, Kevinen_GB
dc.contributor.authorO'Mahony, Edwarden_GB
dc.contributor.authorMacEneaney, Peteren_GB
dc.contributor.authorFitzgerald, Edwarden_GB
dc.contributor.authorMaher, Michael Men_GB
dc.date.accessioned2012-01-31T16:39:01Z-
dc.date.available2012-01-31T16:39:01Z-
dc.date.issued2012-01-31T16:39:01Z-
dc.identifier.citationPediatr Radiol. 2009 Oct;39(10):1095-7. Epub 2009 Jun 23.en_GB
dc.identifier.issn1432-1998 (Electronic)en_GB
dc.identifier.issn0301-0449 (Linking)en_GB
dc.identifier.pmid19547962en_GB
dc.identifier.doi10.1007/s00247-009-1324-4en_GB
dc.identifier.urihttp://hdl.handle.net/10147/206376-
dc.description.abstractNecrotizing fasciitis (NF) is an uncommon soft-tissue infection in children that carries a high mortality rate. We present a 15-year-old girl with chronic pancytopenia secondary to Fanconi anaemia who developed extensive NF of the lower limb, which unfortunately resulted in a fatal outcome. Immunodeficiency is a known risk factor for the development of this condition. The findings in this case demonstrate that patients with Fanconi anaemia may be susceptible to NF and that the clinical course may be more aggressive due to underlying immunosuppression. Prompt diagnosis of NF is vital in order to initiate appropriate treatment and to optimize patient outcome. Radiological investigation demonstrated extensive soft-tissue gas and destruction affecting the entire lower limb, abdominal wall and retroperitoneum, which led to timely definitive diagnosis and management.en_GB
dc.language.isoengen_GB
dc.subject.meshAdolescenten_GB
dc.subject.meshFanconi Anemia/*complications/*radiographyen_GB
dc.subject.meshFasciitis, Necrotizing/*complications/*radiographyen_GB
dc.subject.meshFatal Outcomeen_GB
dc.subject.meshFemaleen_GB
dc.subject.meshHumansen_GB
dc.subject.meshLeg/*radiographyen_GB
dc.subject.meshRetroperitoneal Space/*radiographyen_GB
dc.titleFulminant limb and retroperitoneal necrotizing fasciitis in a 15-year-old girl with Fanconi anaemia.en_GB
dc.contributor.departmentDepartment of Radiology, Mercy University Hospital, Cork, Republic of Ireland., kevin.oregan@ucc.ieen_GB
dc.identifier.journalPediatric radiologyen_GB
dc.description.provinceMunster-

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